
Galya Atanasova
, Medical University Pleven, BulgariaTitle : Situs Inversus With Levocardia and Congenitally Corrected Transposition of Great Vessels in a 45 Year Old Female: A Case Report
Abstract
Introduction
Congenitally corrected transposition of
the great arteries (CCTGA) is a rare cardiac anomaly.
History
and clinical presentation
A 45-year-old female presenting to the
University Hospital with acute onset shortness of breath. She was visibly
cyanotic and had a Class III Dyspnea. Physical examination revealed an
irregular rhythm with heart rate at 90/min, a grade III systolic ejection
murmur and blood pressure was 95/75 mmHg in both arms with normal distal
pulses.
Diagnosis: Chest
X-ray showed a left heart axis, a right-sided gastric bubble below the right
diaphragm and left-sided hepatic contour. Cardiac catheterization was
performed.Transesophageal echocardiogram (TEE) confirmed the diagnosis.
Treatment:
1/congenitally corrected transposition of
the great arteries.
2/medications.
Heart – lung transplantation is the treatment of choice.
Conclusion
The CCTGA is a rare congenital cardiac
anomaly which occurs in less than one percent of all forms of congenital heart
disease. Most cases are Situs Solitus, therefore, the combination of CCTGA and
situs inversus with levocardia are extremely rare defects, especially in
adulthood. Thus, the anatomic repair is not always suitable for older patients.
International papers have published very few cases of adult patients with CCTGA
with situs inversus and other associated defects, so management of these
patients; particularly complicated cases remain controversial.
Biography
Assistant Professor at Medical University Pleven